| Ackerman syndrome | |
|---|---|
| Other names | Pyramidal molar-glaucoma-upper abnormal lip syndrome, interstitial granulomatous dermatitis with arthritis (IGDA) |
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| Ackerman syndrome is inherited in an autosomal recessive manner | |
Ackerman syndrome or interstitial granulomatous dermatitis is a familial syndrome of fused molar roots with a single canal (taurodontism), hypotrichosis, full upper lip without a cupid's bow, thickened and wide philtrum, and occasional juvenile glaucoma. It was described by James L. Ackerman, A. Leon Ackerman, and A. Bernard Ackerman.
Signs and symptoms
- Fused molar roots
- Single root canal
- Juvenile glaucoma
- Sparse body hair
- Distinct facial features: full upper lip, absence of cupid's bow, thick philtrum
- Syndactyly
- Increased pigmentation of finger joints
- Clinodactyly of fifth finger.