Congenital self-healing reticulohistiocytosis
Congenital self-healing reticulohistiocytosis
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| Congenital self-healing reticulohistiocytosis | |
|---|---|
| Other names | Hashimoto–Pritzker disease, and Hashimoto–Pritzker syndrome |
| Specialty | Dermatology |
Congenital self-healing reticulohistiocytosis is a condition that is a self-limited form of Langerhans cell histiocytosis.
Symptoms
Non-specific inflammatory response, which includes fever, lethargy, and weight loss. This is suspected of being a genetic disorder, and as the name implies, is self healing.
- Skin: Commonly seen are a rash which varies from scaly erythematous lesions to red papules pronounced in intertriginous areas. Up to 80% of patients have extensive eruptions on the scalp.
- Lymph node: Enlargement of the lymph nodes in 50% of Histiocytosis cases.
Diagnosis
Treatment
History
It was first described by Ken Hashimoto and M. S. Pritzkar in 1973.
See also
External links
| Classification | |
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| External resources |