Multifocal fibrosclerosis
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| Multifocal fibrosclerosis | |
|---|---|
| Other names | Idiopathic fibrosclerosis |
| Multifocal fibrosclerosis is inherited in an autosomal recessive manner | |
Multifocal fibrosclerosis and idiopathic fibrosclerosis are disorders of unknown aetiology, characterised by fibrous lesions (co-)occurring at a variety of sites. Known manifestations include retroperitoneal fibrosis, mediastinal fibrosis and Riedel's thyroiditis.
They are now considered to be manifestations of IgG4-related disease.